91298

3-Hydroxyisovaleryl-L-carnitine

analytical standard

• Synonim(y): (2R)-3-Carboxy-2-(3-hydroxy-3-methyl-1-oxobutoxy)-N,N,N-trimethyl-1-propanaminium inner salt
• Wzór empiryczny (zapis Hilla): C₁₂H₂₃NO₅
• Numer CAS: 99159-87-2
• Masa cząsteczkowa: 261.31
• Beilstein: 10549761
• Kod UNSPSC: 41116107
• NACRES: NA.24

Właściwości

• klasa czystości: analytical standard
• Poziom jakości: 100
• Próba: ≥90.0% (HPLC)
• aktywność optyczna: [α]/D -17.0±2.0°, c = 0.1 in H₂O
• okres trwałości: limited shelf life, expiry date on the label
• zanieczyszczenia: ≤15% water (calc. on elemental analysis)
• Zastosowanie: clinical testing
• Format: neat
• temp. przechowywania: 2-8°C
• ciąg SMILES: C[N+](C)(C)C[C@H](OC(CC(C)(O)C)=O)CC([O-])=O
• InChI: 1S/C12H23NO5/c1-9(2)6-11(16)18-12(17,7-10(14)15)8-13(3,4)5/h9,17H,6-8H2,1-5H3
• Klucz InChI: DHRNMNHPSWBJEN-UHFFFAOYSA-N

Opis

Działania biochem./fizjol.

3-Hydroxyisovaleryl-L-carnitine is an endogenous metabolite that can result from impairment in the leucine catabolic pathway. 3-Hydroxyisovaleryl-L-carnitine was observed in plasma and urine of patient with isolated 3-methylcrotonyl-CoA carboxylase deficiency and is used as biomarker of biotin deficiency in humans and other metabolic disorders.

Polecane produkty

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Informacja o środkach bezpieczeństwa

• Kod klasy składowania: 11 - Combustible Solids
• Klasa zagrożenia wodnego (WGK): WGK 3
• Temperatura zapłonu (°F): Not applicable
• Temperatura zapłonu (°C): Not applicable