91298

3-Hydroxyisovaleryl-L-carnitine

analytical standard

• Sinonimo/i: (2R)-3-Carboxy-2-(3-hydroxy-3-methyl-1-oxobutoxy)-N,N,N-trimethyl-1-propanaminium inner salt
• Formula empirica (notazione di Hill): C₁₂H₂₃NO₅
• Numero CAS: 99159-87-2
• Peso molecolare: 261.31
• Beilstein: 10549761
• Codice UNSPSC: 41116107
• NACRES: NA.24

Proprietà

• Grado: analytical standard
• Livello qualitativo: 100
• Saggio: ≥90.0% (HPLC)
• Attività ottica: [α]/D -17.0±2.0°, c = 0.1 in H₂O
• Durata: limited shelf life, expiry date on the label
• Impurezze: ≤15% water (calc. on elemental analysis)
• applicazioni: clinical testing
• Formato: neat
• Temperatura di conservazione: 2-8°C
• Stringa SMILE: C[N+](C)(C)C[C@H](OC(CC(C)(O)C)=O)CC([O-])=O
• InChI: 1S/C12H23NO5/c1-9(2)6-11(16)18-12(17,7-10(14)15)8-13(3,4)5/h9,17H,6-8H2,1-5H3; DHRNMNHPSWBJEN-UHFFFAOYSA-N

Descrizione

Azioni biochim/fisiol

3-Hydroxyisovaleryl-L-carnitine is an endogenous metabolite that can result from impairment in the leucine catabolic pathway. 3-Hydroxyisovaleryl-L-carnitine was observed in plasma and urine of patient with isolated 3-methylcrotonyl-CoA carboxylase deficiency and is used as biomarker of biotin deficiency in humans and other metabolic disorders.

Prodotti consigliati

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Informazioni sulla sicurezza

• Codice della classe di stoccaggio: 11 - Combustible Solids
• Classe di pericolosità dell'acqua (WGK): WGK 3
• Punto d’infiammabilità (°F): Not applicable
• Punto d’infiammabilità (°C): Not applicable