91298

3-Hydroxyisovaleryl-L-carnitin

analytical standard

• Synonym(e): (2R)-3-Carboxy-2-(3-hydroxy-3-methyl-1-oxobutoxy)-N,N,N-trimethyl-1-propanaminium Inneres Salz
• Empirische Formel (Hill-System): C₁₂H₂₃NO₅
• CAS-Nummer: 99159-87-2
• Molekulargewicht: 261.31
• Beilstein: 10549761
• UNSPSC-Code: 41116107
• NACRES: NA.24

Eigenschaften

• Qualität: analytical standard
• Qualitätsniveau: 100
• Assay: ≥90.0% (HPLC)
• Optische Aktivität: [α]/D -17.0±2.0°, c = 0.1 in H₂O
• Haltbarkeit: limited shelf life, expiry date on the label
• Verunreinigungen: ≤15% water (calc. on elemental analysis)
• Anwendung(en): clinical testing
• Format: neat
• Lagertemp.: 2-8°C
• SMILES String: C[N+](C)(C)C[C@H](OC(CC(C)(O)C)=O)CC([O-])=O
• InChI: 1S/C12H23NO5/c1-9(2)6-11(16)18-12(17,7-10(14)15)8-13(3,4)5/h9,17H,6-8H2,1-5H3
• InChIKey: DHRNMNHPSWBJEN-UHFFFAOYSA-N

Beschreibung

Biochem./physiol. Wirkung

3-Hydroxyisovaleryl-L-carnitine is an endogenous metabolite that can result from impairment in the leucine catabolic pathway. 3-Hydroxyisovaleryl-L-carnitine was observed in plasma and urine of patient with isolated 3-methylcrotonyl-CoA carboxylase deficiency and is used as biomarker of biotin deficiency in humans and other metabolic disorders.

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Sicherheitshinweise

• Lagerklassenschlüssel: 11 - Combustible Solids
• WGK: WGK 3
• Flammpunkt (°F): Not applicable
• Flammpunkt (°C): Not applicable