SAB1300548

Anti-PYGM (center) antibody produced in rabbit

Ig fraction of antiserum, buffered aqueous solution

• Sinónimos: Anti-Glycogen phosphorylase, Anti-Muscle form, Anti-Myophosphorylase, Anti-PYGM
• UNSPSC Code: 12352203
• NACRES: NA.41

Propiedades

• biological source: rabbit
• Quality Level: 100
• conjugate: unconjugated
• antibody form: Ig fraction of antiserum
• antibody product type: primary antibodies
• clone: polyclonal
• form: buffered aqueous solution
• species reactivity: human
• technique(s): indirect ELISA: 1:1000; western blot: 1:100-1:500
• NCBI accession no.: NP_005600
• UniProt accession no.: P11217
• shipped in: dry ice
• storage temp.: −20°C
• target post-translational modification: unmodified
• Gene Information: human ... PYGM(5834)

Descripción

General description

PYGM catalyzes and regulates the breakdown of glycogen to glucose-1-phosphate. Defects in PYGM are the cause of glycogen storage disease type 5 (GSD5), also known as McArdle disease. GSD5 is a metabolic disorder resulting in myopathy characterized by exercise intolerance, cramps, muscle weakness and recurrent myoglobinuria.

Immunogen

PYGM (NP_005600, 522-556)
This antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide selected from the center region of human PYGM.

Physical form

Purified polyclonal antibody supplied in PBS with 0.09% (W/V) sodium azide.

Información de seguridad

• Storage Class: 10 - Combustible liquids
• wgk_germany: nwg
• flash_point_f: Not applicable
• flash_point_c: Not applicable