HIBADH
3-hydroxyisobutyrate dehydrogenase
Synonyms:
NS5ATP1
Species:
Human HIBADH (11112), Mouse Hibadh (58875), Rat Hibadh (63938), chicken HIBADH (420632), cow HIBADH (512002), Horse HIBADH (100054707), domestic cat HIBADH (101080519), dog HIBADH (479610), sheep HIBADH (101113492), domestic guinea pig Hibadh (100718204)
UniProtKB ID:
Gene ID:
- Human(11112) Summary: This gene encodes a mitochondrial 3-hydroxyisobutyrate dehydrogenase enzyme. The encoded protein plays a critical role in the catabolism of L-valine by catalyzing the oxidation of 3-hydroxyisobutyrate to methylmalonate semialdehyde. [provided by RefSeq, Nov 2011]
- Mouse(58875) 3-hydroxyisobutyrate dehydrogenase
- Rat(63938) 3-hydroxyisobutyrate dehydrogenase
- chicken(420632) 3-hydroxyisobutyrate dehydrogenase
- cow(512002) 3-hydroxyisobutyrate dehydrogenase
- Horse(100054707) 3-hydroxyisobutyrate dehydrogenase
- domestic cat(101080519) 3-hydroxyisobutyrate dehydrogenase
- dog(479610) 3-hydroxyisobutyrate dehydrogenase
- sheep(101113492) 3-hydroxyisobutyrate dehydrogenase
- domestic guinea pig(100718204) 3-hydroxyisobutyrate dehydrogenase
- naked mole-rat(101705721) 3-hydroxyisobutyrate dehydrogenase
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