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Merck

BBOX1

butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1

Synonyms:
BBH, BBOX, G-BBH, gamma-BBH
Species:
Human BBOX1 (8424), Mouse Bbox1 (170442), Rat Bbox1 (64564), Zebrafish bbox1 (572649), chicken BBOX1 (426932), cow BBOX1 (507159), Horse BBOX1 (100072253), domestic cat BBOX1 (101082182), dog BBOX1 (476894), naked mole-rat Bbox1 (101702765) ...More
UniProtKB ID:
O75936, B2R8L7, D3DQZ1, Q6IBJ2
Gene ID:
  • Human(8424) Summary: This gene encodes gamma butyrobetaine hydroxylase which catalyzes the formation of L-carnitine from gamma-butyrobetaine, the last step in the L-carnitine biosynthetic pathway. Carnitine is essential for the transport of activated fatty acids across the mitochondrial membrane during mitochondrial beta-oxidation. [provided by RefSeq, Jul 2008]
  • Mouse(170442) butyrobetaine (gamma), 2-oxoglutarate dioxygenase 1 (gamma-butyrobetaine hydroxylase)
  • Rat(64564) butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
  • Zebrafish(572649) butyrobetaine (gamma), 2-oxoglutarate dioxygenase 1 (gamma-butyrobetaine hydroxylase)
  • chicken(426932) butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
  • cow(507159) butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
  • Horse(100072253) butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
  • domestic cat(101082182) butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
  • dog(476894) butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
  • naked mole-rat(101702765) butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
  • domestic guinea pig(100724732) butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
  • sheep(101115823) butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
  • Domestic Rabbit(100356171) butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1

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