Combined replacement effects of human modified β-hexosaminidase B and GM2 activator protein on GM2 gangliosidoses fibroblasts.

Combined replacement effects of human modified β-hexosaminidase B and GM2 activator protein on GM2 gangliosidoses fibroblasts.

Biochemistry and biophysics reports (2016-06-08)

Keisuke Kitakaze, Chikako Tasaki, Youichi Tajima, Takatsugu Hirokawa, Daisuke Tsuji, Hitoshi Sakuraba, Kohji Itoh

PMID28955902

초록

GM2 gangliosidoses are autosomal recessive lysosomal storage diseases (LSDs) caused by mutations in the

MATERIALS

제품 번호

브랜드

제품 설명

A5316

Sigma-Aldrich

Monoclonal Anti-β-Actin antibody produced in mouse, clone AC-74, ascites fluid

HPA008063

Sigma-Aldrich

Anti-GM2A antibody produced in rabbit, Prestige Antibodies^® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution