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Merck

CFTR

cystic fibrosis transmembrane conductance regulator (ATP-binding cassette sub-family C, member 7)

동의어:
ABC35, ABCC7, CF, CFTR/MRP, MRP7, TNR-CFTR, dJ760C5.1
종:
UniProtKB ID:
Clone ID:
  • Human(1080) Summary: This gene encodes a member of the ATP-binding cassette (ABC) transporter superfamily. ABC proteins transport various molecules across extra- and intra-cellular membranes. ABC genes are divided into seven distinct subfamilies (ABC1, MDR/TAP, MRP, ALD, OABP, GCN20, White). This protein is a member of the MRP subfamily that is involved in multi-drug resistance. The encoded protein functions as a chloride channel and controls the regulation of other transport pathways. Mutations in this gene are associated with the autosomal recessive disorders cystic fibrosis and congenital bilateral aplasia of the vas deferens. Alternatively spliced transcript variants have been described, many of which result from mutations in this gene. [provided by RefSeq, Jul 2008]
  • Mouse(12638) cystic fibrosis transmembrane conductance regulator
  • Rat(24255) cystic fibrosis transmembrane conductance regulator
  • Zebrafish(559080) cystic fibrosis transmembrane conductance regulator, ATP-binding cassette (sub-family C, member 7)
  • chicken(100049619) cystic fibrosis transmembrane conductance regulator (ATP-binding cassette sub-family C, member 7)
  • dog(492302) cystic fibrosis transmembrane conductance regulator (ATP-binding cassette sub-family C, member 7)
  • domestic cat(492308) cystic fibrosis transmembrane conductance regulator (ATP-binding cassette sub-family C, member 7)
  • cow(281067) cystic fibrosis transmembrane conductance regulator (ATP-binding cassette sub-family C, member 7)
  • Horse(100071259) cystic fibrosis transmembrane conductance regulator (ATP-binding cassette sub-family C, member 7)
  • naked mole-rat(101709472) cystic fibrosis transmembrane conductance regulator (ATP-binding cassette sub-family C, member 7)
  • domestic guinea pig(100135647) cystic fibrosis transmembrane conductance regulator homolog
  • domestic guinea pig(100719898) cystic fibrosis transmembrane conductance regulator (ATP-binding cassette sub-family C, member 7)
  • sheep(443347) cystic fibrosis transmembrane conductance regulator (ATP-binding cassette sub-family C, member 7)
  • Domestic Rabbit(100009471) cystic fibrosis transmembrane conductance regulator (ATP-binding cassette sub-family C, member 7)

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Antibodies

제품 번호
설명
종별 반응성
응용분야
Anti-Cystic Fibrosis Transmembrane Conductance Regulator Antibody, a.a. 386-412, clone L12B4, clone L12B4, Chemicon®, from mouse,
종별 반응성
human
응용분야
immunocytochemistry
immunoprecipitation (IP)

western blot
Anti-CFTR Antibody, clone MM13-4, clone MM13-4, Upstate®, from mouse,
종별 반응성
human
응용분야
immunocytochemistry
immunoprecipitation (IP)

western blot
Anti-Cystic Fibrosis Transmembrane Conductance Regulator Antibody, clone MM13-4, clone MM13-4, Chemicon®, from mouse,
종별 반응성
human
응용분야
immunocytochemistry
immunoprecipitation (IP)

western blot
Anti-CFTR Antibody, clone MM13-4 ZooMAb® Mouse Monoclonal, recombinant, expressed in HEK 293 cells,
종별 반응성
human, monkey, porcine
응용분야
flow cytometry
immunocytochemistry

western blot
Anti-CFTR antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution,
종별 반응성
human
응용분야
immunohistochemistry

esiRNA

제품 번호
설명
MISSION® esiRNA, targeting human CFTR,
human
MISSION® esiRNA, targeting mouse Cftr,
mouse