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Merck

CFTR

cystic fibrosis transmembrane conductance regulator (ATP-binding cassette sub-family C, member 7)

Synonyme:
ABC35, ABCC7, CF, CFTR/MRP, MRP7, TNR-CFTR, dJ760C5.1
Spezies:
UniProtKB-ID:
Gen-ID:
  • Human(1080) Summary: This gene encodes a member of the ATP-binding cassette (ABC) transporter superfamily. ABC proteins transport various molecules across extra- and intra-cellular membranes. ABC genes are divided into seven distinct subfamilies (ABC1, MDR/TAP, MRP, ALD, OABP, GCN20, White). This protein is a member of the MRP subfamily that is involved in multi-drug resistance. The encoded protein functions as a chloride channel and controls the regulation of other transport pathways. Mutations in this gene are associated with the autosomal recessive disorders cystic fibrosis and congenital bilateral aplasia of the vas deferens. Alternatively spliced transcript variants have been described, many of which result from mutations in this gene. [provided by RefSeq, Jul 2008]
  • Mouse(12638) cystic fibrosis transmembrane conductance regulator
  • Rat(24255) cystic fibrosis transmembrane conductance regulator
  • Zebrafish(559080) cystic fibrosis transmembrane conductance regulator, ATP-binding cassette (sub-family C, member 7)
  • chicken(100049619) cystic fibrosis transmembrane conductance regulator (ATP-binding cassette sub-family C, member 7)
  • dog(492302) cystic fibrosis transmembrane conductance regulator (ATP-binding cassette sub-family C, member 7)
  • domestic cat(492308) cystic fibrosis transmembrane conductance regulator (ATP-binding cassette sub-family C, member 7)
  • cow(281067) cystic fibrosis transmembrane conductance regulator (ATP-binding cassette sub-family C, member 7)
  • Horse(100071259) cystic fibrosis transmembrane conductance regulator (ATP-binding cassette sub-family C, member 7)
  • naked mole-rat(101709472) cystic fibrosis transmembrane conductance regulator (ATP-binding cassette sub-family C, member 7)
  • domestic guinea pig(100135647) cystic fibrosis transmembrane conductance regulator homolog
  • domestic guinea pig(100719898) cystic fibrosis transmembrane conductance regulator (ATP-binding cassette sub-family C, member 7)
  • sheep(443347) cystic fibrosis transmembrane conductance regulator (ATP-binding cassette sub-family C, member 7)
  • Domestic Rabbit(100009471) cystic fibrosis transmembrane conductance regulator (ATP-binding cassette sub-family C, member 7)

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Antibodies

Produktnummer
Beschreibung
Speziesreaktivität
Anwendung
Anti-CFTR antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution,
Speziesreaktivität
human
Anwendung
immunohistochemistry
Anti-CFTR-Antikörper, Klon MM13-4, clone MM13-4, Upstate®, from mouse,
Speziesreaktivität
human
Anwendung
immunocytochemistry
immunoprecipitation (IP)

western blot
Anti-CFTR-Antikörper, A.S. 1370-1380, Klon M3A7, clone M3A7, Chemicon®, from mouse,
Speziesreaktivität
human
Anwendung
immunocytochemistry
immunoprecipitation (IP)

western blot
Anti-CFTR-Antikörper, Klon M3A7, clone M3A7, Upstate®, from mouse,
Speziesreaktivität
human
Anwendung
immunohistochemistry
immunoprecipitation (IP)

western blot
Anti-CFTR Antibody, clone MM13-4 ZooMAb® Mouse Monoclonal, recombinant, expressed in HEK 293 cells,
Speziesreaktivität
human, monkey, porcine
Anwendung
flow cytometry
immunocytochemistry

western blot

esiRNA

Produktnummer
Beschreibung
Spezies
MISSION® esiRNA, targeting human CFTR,
Spezies
human
MISSION® esiRNA, targeting mouse Cftr,
Spezies
mouse